LymphedemaV1, Main, Exploration, bibRecord, 009D27

Severe Lower Limbs Lymphedema of Late Onset Revealing Polysplenia Syndrome

Identifieur interne : 009D27 ( Main/Exploration ); précédent : 009D26; suivant : 009D28

Severe Lower Limbs Lymphedema of Late Onset Revealing Polysplenia Syndrome

Auteurs : Brigitte Granel ; Jacques Serratrice ; Valérie Juhan ; Pierre Champsaur ; Claude Weiller-Merli ; Xavier Pache ; Laure Swiader ; Patrick Disdier ; Pierre-Jean Weiller

Source :

Angiology [ 0003-3197 ] ; 2001-06.

RBID : ISTEX:454E90F3D5575FB009D1E516153FD7C152077F3C

Descripteurs français

KwdFr :
- Adulte, Diagnostic différentiel, Femelle, Foie (malformations), Humains, Indice de gravité médicale, Jambe, Lymphoedème (étiologie), Maladie chronique, Malformations de l'appareil digestif, Malformations multiples (diagnostic), Médiastin (malformations), Rate (malformations), Syndrome, Système cardiovasculaire (physiopathologie), Tomodensitométrie, Veine cave inférieure (malformations), Veine porte (malformations).
MESH :
- diagnostic : Malformations multiples.
- malformations : Foie, Médiastin, Rate, Veine cave inférieure, Veine porte.
- physiopathologie : Système cardiovasculaire.
- étiologie : Lymphoedème.
- Adulte, Diagnostic différentiel, Femelle, Humains, Indice de gravité médicale, Jambe, Maladie chronique, Malformations de l'appareil digestif, Syndrome, Tomodensitométrie.
Pascal (Inist)
- Etude cas, Forme clinique, Homme, Indice gravité, Lymphoedème, Membre inférieur, Polysplénie.
Wicri :
- topic : Homme.

English descriptors

KwdEn :
- Abnormalities, Multiple (diagnosis), Adult, Cardiovascular System (physiopathology), Case study, Chronic Disease, Clinical form, Diagnosis, Differential, Digestive System Abnormalities, Female, Human, Humans, Leg, Liver (abnormalities), Lower limb, Lymphedema, Lymphedema (etiology), Mediastinum (abnormalities), Polysplenia, Portal Vein (abnormalities), Severity of Illness Index, Severity score, Spleen (abnormalities), Syndrome, Tomography, X-Ray Computed, Vena Cava, Inferior (abnormalities).
MESH :
- abnormalities : Liver, Mediastinum, Portal Vein, Spleen, Vena Cava, Inferior.
- diagnosis : Abnormalities, Multiple.
- etiology : Lymphedema.
- physiopathology : Cardiovascular System.
- Adult, Chronic Disease, Diagnosis, Differential, Digestive System Abnormalities, Female, Humans, Leg, Severity of Illness Index, Syndrome, Tomography, X-Ray Computed.

Abstract

Polysplenia syndrome includes a group of congenital abnormalities involving the spleen, gastrointestinal tract, liver, and cardiovascular system. A case of severe lower limbs lymphedema occurring in a young woman with polysplenia, azygous continuation of the inferior vena cava, short pancreas, and preduodenal portal vein is reported. Lower limb lymphedema could represent a new clinical manifestation associated with polysplenia syndrome. Lymphedema could be the result of a primary anomaly of the lymphatic system or be induced by high pressure in the venous system or by compression of the lymphatic circulation by the hypertrophic azygous vessels in the posterior mediastinum.

Url:

https://api.istex.fr/document/454E90F3D5575FB009D1E516153FD7C152077F3C/fulltext/pdf

DOI: 10.1177/000331970105200608

Affiliations:

Le document en format XML

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<term>Case study</term>
<term>Chronic Disease</term>
<term>Clinical form</term>
<term>Diagnosis, Differential</term>
<term>Digestive System Abnormalities</term>
<term>Female</term>
<term>Human</term>
<term>Humans</term>
<term>Leg</term>
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<term>Portal Vein (abnormalities)</term>
<term>Severity of Illness Index</term>
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<term>Humains</term>
<term>Indice de gravité médicale</term>
<term>Jambe</term>
<term>Lymphoedème (étiologie)</term>
<term>Maladie chronique</term>
<term>Malformations de l'appareil digestif</term>
<term>Malformations multiples (diagnostic)</term>
<term>Médiastin (malformations)</term>
<term>Rate (malformations)</term>
<term>Syndrome</term>
<term>Système cardiovasculaire (physiopathologie)</term>
<term>Tomodensitométrie</term>
<term>Veine cave inférieure (malformations)</term>
<term>Veine porte (malformations)</term>
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<term>Mediastinum</term>
<term>Portal Vein</term>
<term>Spleen</term>
<term>Vena Cava, Inferior</term>
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<term>Médiastin</term>
<term>Rate</term>
<term>Veine cave inférieure</term>
<term>Veine porte</term>
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<term>Chronic Disease</term>
<term>Diagnosis, Differential</term>
<term>Digestive System Abnormalities</term>
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<term>Humans</term>
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<term>Diagnostic différentiel</term>
<term>Femelle</term>
<term>Humains</term>
<term>Indice de gravité médicale</term>
<term>Jambe</term>
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<front><div type="abstract" xml:lang="en">Polysplenia syndrome includes a group of congenital abnormalities involving the spleen, gastrointestinal tract, liver, and cardiovascular system. A case of severe lower limbs lymphedema occurring in a young woman with polysplenia, azygous continuation of the inferior vena cava, short pancreas, and preduodenal portal vein is reported. Lower limb lymphedema could represent a new clinical manifestation associated with polysplenia syndrome. Lymphedema could be the result of a primary anomaly of the lymphatic system or be induced by high pressure in the venous system or by compression of the lymphatic circulation by the hypertrophic azygous vessels in the posterior mediastinum.</div>
</front>
</TEI>
<affiliations><list></list>
<tree><noCountry><name sortKey="Champsaur, Pierre" sort="Champsaur, Pierre" uniqKey="Champsaur P" first="Pierre" last="Champsaur">Pierre Champsaur</name>
<name sortKey="Disdier, Patrick" sort="Disdier, Patrick" uniqKey="Disdier P" first="Patrick" last="Disdier">Patrick Disdier</name>
<name sortKey="Granel, Brigitte" sort="Granel, Brigitte" uniqKey="Granel B" first="Brigitte" last="Granel">Brigitte Granel</name>
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<name sortKey="Swiader, Laure" sort="Swiader, Laure" uniqKey="Swiader L" first="Laure" last="Swiader">Laure Swiader</name>
<name sortKey="Weiller Merli, Claude" sort="Weiller Merli, Claude" uniqKey="Weiller Merli C" first="Claude" last="Weiller-Merli">Claude Weiller-Merli</name>
<name sortKey="Weiller, Pierre Jean" sort="Weiller, Pierre Jean" uniqKey="Weiller P" first="Pierre-Jean" last="Weiller">Pierre-Jean Weiller</name>
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Serveur d'exploration sur le lymphœdème

Severe Lower Limbs Lymphedema of Late Onset Revealing Polysplenia Syndrome

Severe Lower Limbs Lymphedema of Late Onset Revealing Polysplenia Syndrome

Source :

Descripteurs français

English descriptors

Abstract

Links toward previous steps (curation, corpus...)

Le document en format XML

Pour manipuler ce document sous Unix (Dilib)

Pour mettre un lien sur cette page dans le réseau Wicri

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